Síndrome de Klippel-Trenaunay: a propósito de tres nuevas observaciones

Gimeno Pita, P.; Pérez Martín, P.; Marco Tello, M.; Rebage Moisés, V.

doi:10.1016/S1695-4033(00)77476-5

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"referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Du naevus variquex ostéohypertropfique" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "M. Klippel" 1 => "P. Trenaunay" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "Arch Gen Med Paris" "fecha" => "1900" "volumen" => "3" "paginaInicial" => "611" "paginaFinal" => "672" ] ] ] ] ] ] 2 => array:3 [ "identificador" => "bib0015" "etiqueta" => "3." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Haemangiectatic hypertrophy of limbs. Congenital phlebarteriectasis and so-called congenital varicose veins" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:1 [ 0 => "F.P. Weber" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "Brit J Child Dis" "fecha" => "1918" "volumen" => "15" "paginaInicial" => "13" "paginaFinal" => "17" ] ] ] ] ] ] 3 => array:3 [ "identificador" => "bib0020" "etiqueta" => "4." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Klippel-Trenaunay syndrome: spectrum and management" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:6 [ 0 => "A.G. Jacob" 1 => "A.J. Driscoll" 2 => "W.J. Shaughnessy" 3 => "A.W. Starson" 4 => "R.P. Clay" 5 => "P. Glovictki" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1016/S0025-6196(11)63615-X" "Revista" => array:6 [ "tituloSerie" => "Mayo Clin Proc" "fecha" => "1998" "volumen" => "73" "paginaInicial" => "28" "paginaFinal" => "36" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9443675" "web" => "Medline" ] ] ] ] ] ] ] ] 4 => array:3 [ "identificador" => "bib0025" "etiqueta" => "5." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Klippel-Trenaunay syndrome: clinical features, complications and management in children" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:2 [ 0 => "M. Samuel" 1 => "L. Spitz" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Brit J Surg" "fecha" => "1995" "volumen" => "82" "paginaInicial" => "757" "paginaFinal" => "761" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/7542989" "web" => "Medline" ] ] ] ] ] ] ] ] 5 => array:3 [ "identificador" => "bib0030" "etiqueta" => "6." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Klippel-Trenaunay syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:6 [ 0 => "S.A. Berry" 1 => "C. Peterson" 2 => "W. Mize" 3 => "K. Bloom" 4 => "C.H. Zachary" 5 => "P. Blasco" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Am J Med Genet" "fecha" => "1998" "volumen" => "79" "paginaInicial" => "319" "paginaFinal" => "326" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/9781914" "web" => "Medline" ] ] ] ] ] ] ] ] 6 => array:3 [ "identificador" => "bib0035" "etiqueta" => "7." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "An unusual neek mass in a fetus with Klippel-Trenaunay-Weber syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "M.K. Yancey" 1 => "D. Lasley" 2 => "D.S. Richards" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "J Ultra-sound Med" "fecha" => "1993" "volumen" => "12" "paginaInicial" => "779" "paginaFinal" => "782" ] ] ] ] ] ] 7 => array:3 [ "identificador" => "bib0040" "etiqueta" => "8." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Klippel-Trenaunay-Weber syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "J.G. Meine" 1 => "R.A. Schwartz" 2 => "C.K. Janniger" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "Pediatric Dermatol" "fecha" => "1997" "volumen" => "60" "paginaInicial" => "127" "paginaFinal" => "132" ] ] ] ] ] ] 8 => array:3 [ "identificador" => "bib0045" "etiqueta" => "9." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Klippel-Trenaunay syndrome associated with intra-abdominal lymphangioma requiring multiple surgical intervention" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:4 [ 0 => "K. Kondo" 1 => "K. Tanaka" 2 => "T. Fujii" 3 => "S. Akita" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "Ann Plastic Surg" "fecha" => "1997" "volumen" => "39" "paginaInicial" => "435" "paginaFinal" => "437" ] ] ] ] ] ] 9 => array:3 [ "identificador" => "bib0050" "etiqueta" => "10." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Hemimegalencephaly, hemihypertrophy and vascular lesions" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:6 [ 0 => "A. Cristaldi" 1 => "F. Vigevano" 2 => "G. Antoniazzi" 3 => "M. Di Capua" 4 => "A. Andreaz-zi" 5 => "G. Morselli" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Eur J Pediatr" "fecha" => "1995" "volumen" => "154" "paginaInicial" => "134" "paginaFinal" => "137" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/7720742" "web" => "Medline" ] ] ] ] ] ] ] ] 10 => array:3 [ "identificador" => "bib0055" "etiqueta" => "11." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Sonographic demostration of widespread uterine angiomatosis in a preg-nant patient with Klippel-Trenaunay-Weber syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:4 [ 0 => "A. Douglas" 1 => "M.D. Richards" 2 => "C. Amelia" 3 => "M.D. Cruz" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "J Ultrasound" "fecha" => "1997" "volumen" => "16" "paginaInicial" => "631" "paginaFinal" => "633" ] ] ] ] ] ] 11 => array:3 [ "identificador" => "bib0060" "etiqueta" => "12." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Prenatal diagnosis of Klippel-Trenaunay-Weber by ultrasound" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "J. Yankowitz" 1 => "D.D. Slage" 2 => "R. Williamson" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Prenat Diagn" "fecha" => "1994" "volumen" => "14" "paginaInicial" => "745" "paginaFinal" => "749" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/7527539" "web" => "Medline" ] ] ] ] ] ] ] ] 12 => array:3 [ "identificador" => "bib0065" "etiqueta" => "13." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Lymphedema reduction by noninvasive complex lymphedema therapy" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:4 [ 0 => "M. Boris" 1 => "S. Weindorf" 2 => "B. Lasinski" 3 => "G. Boris" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1016/S1470-2045(07)70011-6" "Revista" => array:6 [ "tituloSerie" => "Oncology" "fecha" => "1994" "volumen" => "8" "paginaInicial" => "95" "paginaFinal" => "106" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/17267324" "web" => "Medline" ] ] ] ] ] ] ] ] 13 => array:3 [ "identificador" => "bib0070" "etiqueta" => "14." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "A new case of Klippel-Trenaunay-Weber syndrome: evidence of autosomal dominant inheritance" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "J.M. Ceballos-Quintal" 1 => "D. Pinto-Escalante" 2 => "I. Castillo-Zapata" ] ] ] ] ] "host" => array:1 [ 0 => array:2 [ "doi" => "10.1002/(SICI)1096-8628(19960614)63:3<426::AID-AJMG2>3.0.CO;2-P" "Revista" => array:6 [ "tituloSerie" => "Am J Med Genet" "fecha" => "1996" "volumen" => "63" "paginaInicial" => "426" "paginaFinal" => "427" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/8737646" "web" => "Medline" ] ] ] ] ] ] ] ] 14 => array:3 [ "identificador" => "bib0075" "etiqueta" => "15." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "The etiology of the Klippel-Trenaunay syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "P.A. Baskwerville" 1 => "J.S. Ackroyd" 2 => "N.L. Browse" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:6 [ "tituloSerie" => "Ann Surg" "fecha" => "1985" "volumen" => "202" "paginaInicial" => "624" "paginaFinal" => "627" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/2996451" "web" => "Medline" ] ] ] ] ] ] ] ] 15 => array:3 [ "identificador" => "bib0080" "etiqueta" => "16." "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Psychological aspects of the Klippel-Trenaunay syndrome" "autores" => array:1 [ 0 => array:2 [ "etal" => false "autores" => array:3 [ 0 => "H.M. Van Der Ploel" 1 => "M.N.S. Van Der Ploel" 2 => "J.D. Van Der Ploel-Stapert" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:5 [ "tituloSerie" => "J Psychosomatic Res" "fecha" => "1995" "volumen" => "39" "paginaInicial" => "183" "paginaFinal" => "191" ] ] ] ] ] ] ] ] ] ] ] "idiomaDefecto" => "es" "url" => "/16954033/0000005300000004/v1_201307051520/S1695403300774765/v1_201307051520/es/main.assets" "Apartado" => array:4 [ "identificador" => "14234" "tipo" => "SECCION" "es" => array:2 [ "titulo" => "Medicina fetal y neonatología" "idiomaDefecto" => true ] "idiomaDefecto" => "es" ] "PDF" => "https://static.elsevier.es/multimedia/16954033/0000005300000004/v1_201307051520/S1695403300774765/v1_201307051520/es/main.pdf?idApp=UINPBA00005H&text.app=https://analesdepediatria.org/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S1695403300774765?idApp=UINPBA00005H"]

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Se comunican tres nuevas obervaciones de síndrome de Klippel-Trenaunay (SKT) de distinta evolución y extensión, que reúnen criterios diagnósticos, evaluados por examen físico, técnicas de imagen, estudios radiológicos y de laboratorio. La malformación vascular e hipertrofia de tejidos blandos era evidente en los tres casos, en dos de ellos existían lesiones internas y agrandamiento óseo, y en uno anomalías digitales. Se revisan, además, los principales aspectos de esta importante angiodisplasia.

Palabras clave:

Síndrome de Klippel-Trenaunay (SKT)

Malformación vascular

We report three new cases of Klippel-Trenaunay Syndrome (KTS), with differing evolution and involvement, in which the diagnostic criteria were confirmed by physical evaluation, imaging techniques, radiologic and laboratory studies. Vascular malformation and soft tissue hypertrophy were evident in all three patients: two showed internal lesions and bony hypertrophy and one patient showed digital deformities. We review the main features of this important angiodysplasia.

Key words:

Klippel-Trenaunay Syndrome (KTT)

Vascular malformation

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Bibliografía

[1.]

R.A. Silverman.

Hemangiomas y malformaciones vasculares.

Pediatr Clin North Am (ed. esp.), 38 (1991), pp. 835-855

[2.]

M. Klippel, P. Trenaunay.

Du naevus variquex ostéohypertropfique.

Arch Gen Med Paris, 3 (1900), pp. 611-672

[3.]

F.P. Weber.

Haemangiectatic hypertrophy of limbs. Congenital phlebarteriectasis and so-called congenital varicose veins.

Brit J Child Dis, 15 (1918), pp. 13-17

[4.]

A.G. Jacob, A.J. Driscoll, W.J. Shaughnessy, A.W. Starson, R.P. Clay, P. Glovictki.

Klippel-Trenaunay syndrome: spectrum and management.

Mayo Clin Proc, 73 (1998), pp. 28-36

http://dx.doi.org/10.1016/S0025-6196(11)63615-X | Medline

[5.]

M. Samuel, L. Spitz.

Klippel-Trenaunay syndrome: clinical features, complications and management in children.

Brit J Surg, 82 (1995), pp. 757-761

Medline

[6.]

S.A. Berry, C. Peterson, W. Mize, K. Bloom, C.H. Zachary, P. Blasco.

Klippel-Trenaunay syndrome.

Am J Med Genet, 79 (1998), pp. 319-326

Medline

[7.]

M.K. Yancey, D. Lasley, D.S. Richards.

An unusual neek mass in a fetus with Klippel-Trenaunay-Weber syndrome.

J Ultra-sound Med, 12 (1993), pp. 779-782

[8.]

J.G. Meine, R.A. Schwartz, C.K. Janniger.

Klippel-Trenaunay-Weber syndrome.

Pediatric Dermatol, 60 (1997), pp. 127-132

[9.]

K. Kondo, K. Tanaka, T. Fujii, S. Akita.

Klippel-Trenaunay syndrome associated with intra-abdominal lymphangioma requiring multiple surgical intervention.

Ann Plastic Surg, 39 (1997), pp. 435-437

[10.]

A. Cristaldi, F. Vigevano, G. Antoniazzi, M. Di Capua, A. Andreaz-zi, G. Morselli.

Hemimegalencephaly, hemihypertrophy and vascular lesions.

Eur J Pediatr, 154 (1995), pp. 134-137

Medline

[11.]

A. Douglas, M.D. Richards, C. Amelia, M.D. Cruz.

Sonographic demostration of widespread uterine angiomatosis in a preg-nant patient with Klippel-Trenaunay-Weber syndrome.

J Ultrasound, 16 (1997), pp. 631-633

[12.]

J. Yankowitz, D.D. Slage, R. Williamson.

Prenatal diagnosis of Klippel-Trenaunay-Weber by ultrasound.

Prenat Diagn, 14 (1994), pp. 745-749

Medline

[13.]

M. Boris, S. Weindorf, B. Lasinski, G. Boris.

Lymphedema reduction by noninvasive complex lymphedema therapy.

Oncology, 8 (1994), pp. 95-106

http://dx.doi.org/10.1016/S1470-2045(07)70011-6 | Medline

[14.]

J.M. Ceballos-Quintal, D. Pinto-Escalante, I. Castillo-Zapata.

A new case of Klippel-Trenaunay-Weber syndrome: evidence of autosomal dominant inheritance.

Am J Med Genet, 63 (1996), pp. 426-427

http://dx.doi.org/10.1002/(SICI)1096-8628(19960614)63:3<426::AID-AJMG2>3.0.CO;2-P | Medline

[15.]

P.A. Baskwerville, J.S. Ackroyd, N.L. Browse.

The etiology of the Klippel-Trenaunay syndrome.

Ann Surg, 202 (1985), pp. 624-627

Medline

[16.]

H.M. Van Der Ploel, M.N.S. Van Der Ploel, J.D. Van Der Ploel-Stapert.

Psychological aspects of the Klippel-Trenaunay syndrome.

J Psychosomatic Res, 39 (1995), pp. 183-191

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