Trombosis de la vena porta

Senderos Aguirre, B.; García Sanz, M.aC.; Casanova Morcillo, A.

doi:10.1016/S1695-4033(01)77740-5

Article information

La obstrucción de la vena porta con un hígado sano es una causa frecuente de hipertensión portal en los niños. El curso natural de la enfermedad se caracteriza por hemorragias recurrentes durante los primeros años de vida y el desarrollo de esplenomegalia e hiperesplenismo. Debido a que el riesgo de hemorragia puede disminuir con la edad se intenta mantener un tratamiento conservador mientras sea posible.

Se presentan 2 casos de trombosis de la vena porta (TVP) en adolescentes que nunca han presentado sangrado de varices y que con tratamiento conservador se mantienen asintomáticos hasta la actualidad

Palabras clave:

Trombosis de vena porta

Esplenomegalia

Hiperten-sión portal

Cavernoma

Occlusion of the portal vein in patients with normal liver is a frequent cause of hypertension in children. The natural course of the disease is characterized by recurrent bleeding during the first years of life and the development of splenomegaly and hypersplenism. Because the risk of bleeding in these patients can decrease with age, non-aggressive management is preferred whenever possible.

We report two cases of portal vein thrombosis in adolescents with no previous esophageal variceal bleeding. The patients were treated conservatively and, at the present moment, remain symptom-free

Key words:

Portal vein thrombosis

Splenomegaly

Portal hyperten-sion

Cavernoma

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