Original articleClinical features of mesenteric lymphatic malformation in children
Section snippets
Patients and methods
We investigated 25 patients who underwent ML surgery in the Department of Paediatric Surgery, Seoul National University Children’s Hospital from 1991 to 2011. The clinicopathological data, including gender, age, clinical signs and symptoms, preoperative diagnosis, radiological findings, histology, operative findings, operative methods and outcomes, were reviewed retrospectively. To investigate recurrence, we conducted telephone interviews. The median follow-up period was 10.9 ± 6.9 months (2
Clinical features
In total, 11 boys and 14 girls were included in the study, and the ages at diagnosis ranged from 9 months to 12 years (mean: 61 ± 41 months). The duration from the occurrence of the first symptom to the diagnosis was 54 ± 110 days (range: 1 day to 1 year). The observation period from the diagnosis to surgery was 73 ± 265 days (range: 1 day to 3.7 years). The mean weight of the patients was 19 ± 14.5 kg and ranged from 10 kg to 70 kg. Three patients had associated diseases, including a hepatic hemangioma, left
Discussion
MLs occur at all ages, with 25% of the patients diagnosed before they are teenagers. ML is most frequently diagnosed at 30–40 years [13], and nearly 60% of ML patients are diagnosed before their fiftieth year of life [6]. Some studies report that ML is more predominant in males [14]. MLs could exist anywhere in the mesentery, from the duodenum to the rectum. The most frequently involved site is the small intestine, particularly the ileum. Ten percent of MLs involve the colon, and the transverse
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