Original articleCongenital heart surgeryMore Than 25 Years of Experience in Managing Pulmonary Atresia With Intact Ventricular Septum
Section snippets
Patients and Data Collection
This descriptive retrospective study was approved by the ethics committee of our institution. We identified all patients diagnosed with or treated for PAIVS in our institution between January 1, 1985 and December 31, 2011. A total of 60 patients were included in this study. For each patient, available medical records, echocardiograms, angiograms, and operative reports were reviewed. Patients’ clinical characteristics at first presentation are shown in Table 1.
Morphologic Subgroups
Patients were categorized into 1 of
Results
Follow-up data were complete for 59 of 60 patients. One patient returned to his country of origin after definitive repair was achieved. For the total study population, median follow-up time from the date of first hospital admission was 9.8 years (range, 2 days–25.9 years). For surviving patients with complete follow-up, it was 11.2 years (range, 9 months–25.9 years).
Comment
For the total series of 60 patients, estimated overall survival at 1, 5, and 15 years after initial admission was 88.3%, 86.5%, and 86.5%, respectively. This is congruent with other studies that reported most patients with PAIVS die within the first years of life 2, 3, 7, 10. All deaths except 1 in our series were early postprocedure deaths. The last death occurred in the year 2000, suggesting improved surgical or perioperative treatment, or both. Variable survival rates have been reported in
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